A 55-year-old Turkish man with a history of chronic hepatitis B for
35 years, presented with incapacitating fatigue and worsening shortness
of breath. He was hospitalized several times because of hepatic encephalopathy.
He underwent liver transplantation for a clinical diagnosis of Child's
C cirrhosis complicated by hepatopulmonary syndrome. The explanted liver,
however, was not cirrhotic and demonstrated features of hepatoportal sclerosis.
Although treatment for hepatoportal sclerosis is relief of portal hypertension;
in rare cases such as in this patient with liver failure, liver transplantation
is indicated.
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